Table 3. Results of complement exploration at the time of diagnosis

CaseFactor H Antigenic Levelsa (70 to 130%)C3a (660 to 1250 mg/L)Factor Ba (90 to 320 mg/L)CH50a (70 to 130%)C4a (93 to 320 mg/L)
a Normal values are indicated in parenthesis.
b In italics are indicated results obtained under FFP therapy.
c FH functional activity = 50%.
1<1501724328
2<17015<10384
3<117070<10600
4<110050<10250
5<1<4012<10263
6<1<4017<10133
75058019098320
83531020068250
9454307971220
103024025059370
11452708062140
12b41/94453/78360/13983/103215/151
13373825561237
1494c47017072230
1555834103124256
16 (Father)5281215093160
16 (Mother)46799182136205