Table 2.

Results of complement investigation of the three patients at different selected timesa

TestsPatient 1Patient 2Patient 3Normal Ranges
Day 0Day 15Month 7Month 14Month 17Month 2Month 15Month 27Month 3Month 24Month 29
CH506993809685919411782788670–130%
C3460638610647630978785771594574630660–1250 mg/L
C41301631168811212918815617612712493–380 mg/L
Factor B6878766976169158147112908290–320 mg/L
FH antigen91NDND121951001171099512810970–130%
FH activity10ND213847NDND70ND566770–130%
Anti-FH IgG23231812110784295531715931162183019102160<1 AUb/ml
  • a ND, not determined.

  • b Arbitrary units as defined by a reference positive plasma that was issue from a sample of patient 1 taken at month 6 of follow up.