Table 1.

Antenatal characteristics of patients with ARPKD (n = 12)a

PatientGA (wk)AFFamily HistoryPerinatal OutcomeKidney Length (SD)CystsCMD
129MOHNoAlive+3NoP
226SOHNoTOP+3NoP
326SOHNoTOP+3NoP
422MOHARPKDTOP+3NoP
532MOHNoTOP+4NoP
622SOHNoTOP+3NoP
726SOHNoTOP+2NoP
828SOHNoTOP+3NoP
932MOHNoTOP+3NoP
1022MOHNoTOP+2NoP
1124SOHNoTOP+3NoP
1232SOHNoND+4NoP
  • a AF, amniotic fluid volume; ARPKD, autosomal recessive polycystic kidney disease; CMD, corticomedullary differentiation; GA, gestational age; MOH, moderate oligohydramnios; ND, neonatal death; P, poor; SOH, severe oligohydramnios; TOP, termination of pregnancy.