Table 5.

Scoring of podocytes, GL3 inclusions, vacuolization, and composite scores

Patient No.Age (yr)/SexTime (yr)Score Osmicated Toluidine Semithin SectionsScore PAS SectionsComposite Score
No Scorable GlomeruliInclusions (0–4)No Scorable GlomeruliVacuolization (0–3)No Scorable GlomeruliInclusions and Vacuolization (0–7)
17/M034.0313.0347.0
580.13120.25200.4
211/M0234.0292.9526.9
344.0303.0347.0
544.0152.8196.8
311/F034.0323.0357.0
5151.53121.33272.9
412/M0144.0133.0277.0
554.0112.64166.6
516/M−2
0a34.0102.9136.9
142.25101.3143.6
560.67161.1221.8
616/M074.0162.88236.9
3184.0183.0367.0
564.0153.0217.0
717/M−2
0a34.093.0127.0
1214.093.0307.0
544.0143.0187.0
817/M0144.0153.0297.0
1114.0353.0467.0
918/M064.0193.0257.0
124.0153.0177.0
562.33122.58184.9
1023/M044.0163.0207.0
1234.0133.0367.0
514.0163.0177.0
1130/M054.0202.85256.9
134.0243.0277.0
524.0143.0167.0
1233/M−3
0b264.0163.0427.0
5304.0123.0427.0
  • Time, time of biopsy: 0 is baseline, numbers represent years after baseline; M, male; F, female.

  • a Two years of ERT at baseline.

  • b Three years of ERT at baseline.